Congenital Perineal Lipoma-like Lipoblastoma

Congenital Perineal Lipoma-like Lipoblastoma

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Introduction: Adipocytic tumors and its variants are common neoplasms of adults; however, they are rarely seen in paediatric age group, too.Lipoblastoma typically occurs in children and are diagnosed by the presence of a multivacuolated lipoblast.However, things get complicated when one has to search for these lipoblasts in a background of classical lipoma.As a result, such cases are misdiagnosed and managed inappropriately.We report Shipping Protection the first case of a congenital lipoma like lipoblastoma with an unusual presentation.

Case Presentation: A 10-day-old male was admitted to the Paediatric Surgery Outpatient Department with a mass in his perianal region since birth.On examination, the mass was non-tender, pedunculated, and located at the margin of the anal opening.A provisional clinical diagnosis of anal tag was made, and swelling was excised.Grossly, we received a skin covered soft tissue mass measuring 1.2cm in diameter.

The cut section was yellow and had a soft to firm consistency.Histopathological examination showed a well-delineated moderately cellular lesion comprising of lobules of adipocytes in varying stages of maturation; large number of mature adipocytes and few interspersed multivacuolated lipoblasts.A final diagnosis of lipoma-like lipoblastoma was made.Conclusion: Lipoma-like lipoblastoma can be seen as a congenital mass and at unusual sites like the perianal region.An accurate diagnosis of this entity is essential for appropriate management.

Histopathology is the gold 5.45/5CRV standard for diagnosis and calls for increased awareness.